Non-Functional Paraganglioma of Retroperitoneum Mimicking Pancreatic Mass with Concurrent Urinary Bladder Paraganglioma: An Extremely Rare Entity
Published: February 1, 2015 | DOI: https://doi.org/10.7860/JCDR/2015/.5570
Ankur Verma, Diwakar Pandey, Azaz Akhtar, Ashish Arsia, Nain Singh
1. Senior Resident, Department of Surgery, Lady Harding Medical College and SSKH, New Delhi, India.
2. Post graduate student, Department of Surgery, Lady Harding Medical College and SSKH, New Delhi, India.
3. Assistant Professor, Department of Surgery, Lady Harding Medical College and SSKH, New Delhi, India.
4. Associate Professor, Department of Surgery, Lady Harding Medical College and SSKH, New Delhi, India.
5. Associate Professor, Department of Surgery, Lady Harding Medical College and SSKH, New Delhi, India.
Correspondence
Mr. Diwakar Pandey,
HSB 320, Lady Hardinge Medical College and Sskh, Shaheed Bhagat Singh Marg, New Delhi -110001, India.
E-mail: drdiwakarpandey86@gmail.com
Paragangliomas are extra-adrenal tumours of the autonomic nervous system, which rarely present as primary retroperitoneal mass mimicking pancreatic malignancy (incidence 2-8 per million populations). Urinary Bladder Paraganglioma are also extremely rare (0.06% of all Bladder Tumour and 6% of Paragangliomas) with most being malignant and high grade tumours. Non-functional varieties of both tumours are usually incidentally diagnosed. The possibility for malignant transformation in them makes surgical excision the treatment of choice. A 45-year-old lady with abdominal pain was investigated to have a complex retroperitoneal mass behind head of pancreas and a urinary bladder mass. Complete excision of retroperitoneal and bladder lesion was done. Histopathological examinations of both specimens were suggestive of Paraganglioma with no abnormal mitotic activity and capsular/vascular invasion. Although concurrent non functional paragangliomas had been reported but the synchronous non-functional paragangliomas of retroperitoneum and urinary bladder reported in this case is extremely rare and is not reported so far in English literature.
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